Raghib Syndrome is a rare developmental complex, which consists of persistence of the left superior vena cava (PLSVC) along\nwith coronary sinus ostial atresia and atrial septal defect. This Raghib complex anomaly has also been associated with other\ncongenital malformations including ventricular septal defects, enlargement of the tricuspid annulus, and pulmonary stenosis. Our\ncase demonstrates an isolated PLSVC draining into the left atrium along with coronary sinus atresia in a young patient presenting\nwith cryptogenic stroke without the atrial septal defect. Majority of the cases reported in the literature were found to have the\nlesion during the postmortem evaluation or were characterized at angiography and/or echocardiography.We stress the importance\nof modern day imaging like the computed tomography (CT) angiography and cardiac MRI in diagnosis and surgical management\nof such rare lesions leading to cryptogenic strokes.
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